Professor of Pathology, Case West Res University
Pathology
Dr. Pierluigi Gambetti, MD
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Pierluigi Gambetti works in the field of Pathology. He received 1 awards: "America's Top Doctors". Pierluigi Gambetti is a published doctor and has 77 publications published. The lastest was: 'Status spongiosus of rat central nervous system induced by actinomycin D.'
Publications
- Comparative Study of Prions in Iatrogenic and Sporadic Creutzfeldt-Jakob Disease.
- Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis.
- Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old.
- Thermodynamic Stabilization of the Folded Domain of Prion Protein Inhibits Prion Infection in Vivo.
- Glycoform-selective prion formation in sporadic and familial forms of prion disease.
- Protease-sensitive prions with 144-bp insertion mutations.
- Creationism and Evolutionism in Prions.
- Genetic CJD with a novel E200G mutation in the prion protein gene and comparison with E200K mutation cases.
- Assessing prion infectivity of human urine in sporadic creutzfeldt-jakob disease.
- Treatable neurological disorders misdiagnosed as Creutzfeldt-Jakob disease.
- Variably protease-sensitive prionopathy: a novel disease of the prion protein.
- Generation of a new form of human PrP(Sc) in vitro by interspecies transmission from cervid prions.
- Molecular biology and pathology of prion strains in sporadic human prion diseases.
- Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein.
- Characterization of the prion protein in human urine.
- Mammalian prions generated from bacterially expressed prion protein in the absence of any mammalian cofactors.
- Multiorgan detection and characterization of protease-resistant prion protein in a case of variant CJD examined in the United States.
- The role of glycophosphatidylinositol anchor in the amplification of the scrapie isoform of prion protein in vitro.
- Codistribution of amyloid beta plaques and spongiform degeneration in familial Creutzfeldt-Jakob disease with the E200K-129M haplotype.
- Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics.
- Tribute to Robert Terry.
- Failure to detect the presence of prions in the uterine and gestational tissues from a Gravida with Creutzfeldt-Jakob disease.
- Variant Creutzfeldt-Jakob disease: French versus British.
- Toxic effects of intracerebral PrP antibody administration during the course of BSE infection in mice.
- Cell-free propagation of prion strains.
- Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease.
- Sporadic fatal insomnia masquerading as a paraneoplastic cerebellar syndrome.
- A novel human disease with abnormal prion protein sensitive to protease.
- Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain.
- A refined method for molecular typing reveals that co-occurrence of PrP(Sc) types in Creutzfeldt-Jakob disease is not the rule.
- Inducible overexpression of wild-type prion protein in the muscles leads to a primary myopathy in transgenic mice.
- Washington statewide pathology surveillance for prion disease.
- Insoluble aggregates and protease-resistant conformers of prion protein in uninfected human brains.
- Classification of sporadic Creutzfeldt-Jakob disease revisited.
- Soluble amyloid-beta in the brain: the scarlet pimpernel.
- Gerstmann-Sträussler-Scheinker: a new phenotype with 'curly' PrP deposits.
- Pre-symptomatic diagnosis in fatal familial insomnia: serial neurophysiological and 18FDG-PET studies.
- Chronic wasting disease of elk and deer and Creutzfeldt-Jakob disease: comparative analysis of the scrapie prion protein.
- Creutzfeldt-Jakob disease (CJD) with a mutation at codon 148 of prion protein gene: relationship with sporadic CJD.
- Variant Creutzfeldt-Jakob disease death, United States.
- Chronic wasting disease of elk: transmissibility to humans examined by transgenic mouse models.
- beta-amyloid is different in normal aging and in Alzheimer disease.
- Redox metals and oxidative abnormalities in human prion diseases.
- Characterization of the F198S prion protein mutation: enhanced glycosylation and defective refolding.
- From microbes to prions the final proof of the prion hypothesis.
- Biochemical fingerprints of prion diseases: scrapie prion protein in human prion diseases that share prion genotype and type.
- Protease-resistant human prion protein and ferritin are cotransported across Caco-2 epithelial cells: implications for species barrier in prion uptake from the intestine.
- Concealment of epitope by reduction and alkylation in prion protein.
- Expression of excitatory amino acid transporter-1 (EAAT-1) in brain macrophages and microglia of patients with prion diseases.
- Targeting prion amyloid deposits in vivo.
- Chronic wasting disease and potential transmission to humans.
- Soluble amyloid beta-protein is increased in frontotemporal dementia with tau gene mutations.
- Effects of different experimental conditions on the PrPSc core generated by protease digestion: implications for strain typing and molecular classification of CJD.
- Antibody to DNA detects scrapie but not normal prion protein.
- Fatal familial insomnia: the first account in a family of Chinese descent.
- Sporadic and familial CJD: classification and characterisation.
- Identification of novel proteinase K-resistant C-terminal fragments of PrP in Creutzfeldt-Jakob disease.
- Familial and sporadic fatal insomnia.
- Hereditary Creutzfeldt-Jakob disease and fatal familial insomnia.
- Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene.
- Monitoring the occurrence of emerging forms of Creutzfeldt-Jakob disease in the United States.
- Characterization of prion proteins.
- Does the prion protein gene 129 codon polymorphism influence sleep? Evidence from a fatal familial insomnia kindred.
- Intercellular transfer of the cellular prion protein.
- Spontaneous mutations in the prion protein gene causing transmissible spongiform encephalopathy.
- Human prion diseases.
- A journey through the species barrier.
- Heterogeneity of normal prion protein in two- dimensional immunoblot: presence of various glycosylated and truncated forms.
- Biochemical studies of synapses in vitro. I. Protein synthesis.
- [Familial insomnia with a malignant course: a new thalamic disease].
- Cardiovascular dysautonomia in fatal familial insomnia.
- Demonstration of a novel neurofilament associated antigen with the neurofibrillary pathology of Alzheimer and related diseases.
- Amyloidoma of the CNS. II. Immunohistochemical and biochemical study.
- Status spongiosus of rat central nervous system induced by actinomycin D.
- [CLINICO-STATISTICAL CONTRIBUTION TO THE STUDY OF EPILEPTIC MANIFESTATIONS IN BRAIN TUMORS (CONSIDERATIONS OF 882 CASES)].
- [CLINICAL AND ELECTROENCEPHALOGRAPHIC CONSIDERATIONS ON PRESENILE AND SENILE EPILEPSY].
Doctors Specialties
- Neuropathology
- Pathology
Accepted Insurances
Awards
- America's Top Doctors
Hospital
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University Hospitals Case Medical Center
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